Mugii Naoki, Hamaguchi Yasuhito, Maddali-Bongi Susanna
Department of Rehabilitation, Kanazawa University Hospital, Kanazawa - Japan.
Department of Dermatology, School of Medicine, Institute of Medical, Pharmaceutical, and Health Sciences, Kanazawa University, Kanazawa - Japan.
J Scleroderma Relat Disord. 2018 Feb;3(1):71-80. doi: 10.1177/2397198317750043. Epub 2018 Apr 4.
Systemic sclerosis is a multisystem connective tissue disorder characterized by excessive fibrosis of the skin and internal organs. Impairments in skin, the musculoskeletal system, and respiratory system require rehabilitation therapy because they may lead to disabilities and reduce the quality of life in daily activities. Rehabilitation for systemic sclerosis mainly comprises two distinct approaches that include local and global rehabilitation. Local rehabilitation is applied to maintain and/or improve hand and face functions, while global rehabilitation includes aerobic and resistance exercises. Although few high-quality randomized clinical trials have been conducted to date, previous studies indicated the effectiveness of rehabilitation therapy for decreasing local and systemic disabilities, resulting in improved quality of life. Rehabilitation for systemic sclerosis needs to be regularly and constantly performed at home as well as in hospitals. Physicians involved in the treatment of systemic sclerosis need to consider rehabilitation, and skilled physiotherapists and occupational therapists also play a crucial role in evaluating and treating systemic sclerosis patients.
系统性硬化症是一种多系统结缔组织疾病，其特征是皮肤和内脏器官过度纤维化。皮肤、肌肉骨骼系统和呼吸系统的功能障碍需要康复治疗，因为它们可能导致残疾并降低日常活动的生活质量。系统性硬化症的康复主要包括两种不同的方法，即局部康复和整体康复。局部康复用于维持和/或改善手部和面部功能，而整体康复包括有氧运动和抗阻运动。尽管迄今为止很少进行高质量的随机临床试验，但先前的研究表明康复治疗在减少局部和全身残疾方面是有效的，从而提高了生活质量。系统性硬化症的康复需要在家庭和医院定期持续进行。参与系统性硬化症治疗的医生需要考虑康复问题，熟练的物理治疗师和职业治疗师在评估和治疗系统性硬化症患者方面也起着至关重要的作用。
