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平卧呼吸-直立性低氧血症综合征:一种导致体位性呼吸衰竭的罕见病因。

Platypnea-Orthodeoxia Syndrome: A Rare Cause of Positional Respiratory Failure.

作者信息

Soares Pedro R, Melo Nuno, Ferrao Diana, Sousa Estela, Santos Adriana, Gomes André, Friões Fernando

机构信息

Internal Medicine Department, Centro Hospitalar Universitário de São João, Porto, PRT.

Intermediate Care Unit, Internal Medicine Department, Centro Hospitalar Universitário de São João, Porto, PRT.

出版信息

Cureus. 2022 Dec 14;14(12):e32538. doi: 10.7759/cureus.32538. eCollection 2022 Dec.

DOI:10.7759/cureus.32538
PMID:36654653
原文链接:https://pmc.ncbi.nlm.nih.gov/articles/PMC9839979/
Abstract

Platypnea-orthodeoxia syndrome (POS) is a rare clinical entity characterized by dyspnea and arterial desaturation in the upright position. Hypoxia in POS has been attributed to the mixing of deoxygenated venous with oxygenated arterial blood via a shunt, with patent foramen ovale being the most commonly reported abnormality. A systematic evaluation is necessary to identify the underlying cause and promote an appropriate intervention. Here, we present the case of a 79-year-old female with a new diagnosis of POS during the workup of hypoxemic respiratory failure.

摘要

平卧呼吸-直立性低氧血症综合征(POS)是一种罕见的临床病症,其特征为直立位时出现呼吸困难和动脉血氧饱和度降低。POS中的低氧血症被认为是由于脱氧静脉血与氧合动脉血通过分流混合所致,卵圆孔未闭是最常报道的异常情况。进行系统评估以确定潜在病因并促进适当干预是必要的。在此,我们报告一例79岁女性病例,该患者在低氧性呼吸衰竭检查过程中被新诊断为POS。

https://cdn.ncbi.nlm.nih.gov/pmc/blobs/ff22/9839979/8e713340a04c/cureus-0014-00000032538-i02.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/ff22/9839979/ec77dbf57676/cureus-0014-00000032538-i01.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/ff22/9839979/8e713340a04c/cureus-0014-00000032538-i02.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/ff22/9839979/ec77dbf57676/cureus-0014-00000032538-i01.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/ff22/9839979/8e713340a04c/cureus-0014-00000032538-i02.jpg

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引用本文的文献

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Platypnea-Orthodeoxia Syndrome: Manifestation of a Patent Foramen Ovale.平卧呼吸困难-直立性低氧血症综合征:卵圆孔未闭的表现。
Cureus. 2024 Dec 18;16(12):e75970. doi: 10.7759/cureus.75970. eCollection 2024 Dec.

本文引用的文献

1
Platypnea-Orthodeoxia Syndrome After Complicated Cholecystectomy: An Unsuspected Diagnosis.
Acta Med Port. 2017 Nov 29;30(11):827-830. doi: 10.20344/amp.8700.
2
The multiple dimensions of Platypnea-Orthodeoxia syndrome: A review.平卧呼吸-直立性低氧血症综合征的多维度研究:综述
Respir Med. 2017 Aug;129:31-38. doi: 10.1016/j.rmed.2017.05.016. Epub 2017 May 31.
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The platypnea-orthodeoxia syndrome.平卧呼吸-直立性低氧血症综合征
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Cardiac platypnea-orthodeoxia syndrome: an often unrecognized malady.心脏平卧呼吸-直立性低氧血症综合征:一种常未被识别的病症。
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Platypnea-orthodeoxia syndrome in review: defining a new disease?扁平呼吸-直立性低氧血症综合征综述:正在定义一种新疾病?
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Mechanisms of platypnea-orthodeoxia: what causes water to flow uphill?平卧呼吸-直立性低氧血症的机制:是什么导致水向上流动?
Circulation. 2002 Feb 12;105(6):e47.
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Platypnea-orthodeoxia syndrome: etiology, differential diagnosis, and management.平卧呼吸-直立性低氧血症综合征:病因、鉴别诊断及管理
Catheter Cardiovasc Interv. 1999 May;47(1):64-6. doi: 10.1002/(SICI)1522-726X(199905)47:1<64::AID-CCD15>3.0.CO;2-6.
8
Incidence and size of patent foramen ovale during the first 10 decades of life: an autopsy study of 965 normal hearts.出生后第一个十年间卵圆孔未闭的发生率及大小:965例正常心脏的尸检研究
Mayo Clin Proc. 1984 Jan;59(1):17-20. doi: 10.1016/s0025-6196(12)60336-x.