Estacion Mark, Liu Shujun, Cheng Xiaoyang, Dib-Hajj Sulayman, Waxman Stephen G
Department of Neurology and Center for Neuroscience and Regeneration Research, Yale University School of Medicine, New Haven, CT, United States.
Rehabilitation Research Center, Veterans Affairs Connecticut Healthcare System, West Haven, CT, United States.
Front Pharmacol. 2023 Feb 27;14:1138556. doi: 10.3389/fphar.2023.1138556. eCollection 2023.
Chronic pain is highly prevalent and remains a significant unmet global medical need. As part of a search for modulatory genes that confer pain resilience, we have studied two family cohorts where one individual reported much less pain than other family members that share the same pathogenic gain-of-function Nav1.7 mutation that confers hyperexcitability on pain-signaling dorsal root ganglion (DRG) neurons. In each of these kindreds, the pain-resilient individual carried a gain-of-function variant in Kv7.2 or Kv7.3, two potassium channels that stabilize membrane potential and reduce excitability. Our observation in this molecular genetic study that these gain-of-function Kv7.2 and 7.3 variants reduce DRG neuron excitability suggests that agents that activate or open Kv7 channels should attenuate sensory neuron firing. In the present study, we assess the effects on sensory neuron excitability of three Kv7 modulators-retigabine (Kv7.2 thru Kv7.5 activator), ICA-110381 (Kv7.2/Kv7.3 specific activator), and as a comparator ML277 (Kv7.1 specific activator)-in a "human-pain-in-a-dish" model (human iPSC-derived sensory neurons, iPSC-SN). Multi-electrode-array (MEA) recordings demonstrated inhibition of firing with retigabine and ICA-110381 (but not with ML277), with the concentration-response curve indicating that retigabine can achieve a 50% reduction of firing with sub-micromolar concentrations. Current-clamp recording demonstrated that retigabine hyperpolarized iPSC-SN resting potential and increased threshold. This study implicates Kv7.2/Kv7.3 channels as effective modulators of sensory neuron excitability, and suggest that compounds that specifically target Kv7.2/Kv7.3 currents in sensory neurons, including human sensory neurons, might provide an effective approach toward pain relief.
慢性疼痛极为普遍,仍然是全球一项重大的未满足医疗需求。作为寻找赋予疼痛恢复力的调节基因的一部分,我们研究了两个家族队列,其中一个个体报告的疼痛程度远低于其他家族成员,这些家族成员都携带相同的致病性功能获得性Nav1.7突变,该突变会使疼痛信号背根神经节(DRG)神经元产生过度兴奋性。在每个家族中,具有疼痛恢复力的个体在Kv7.2或Kv7.3(两种稳定膜电位并降低兴奋性的钾通道)中携带功能获得性变体。我们在这项分子遗传学研究中的观察结果表明,这些功能获得性Kv7.2和7.3变体降低了DRG神经元的兴奋性,这表明激活或打开Kv7通道的药物应能减弱感觉神经元的放电。在本研究中,我们在“盘中人疼痛”模型(人诱导多能干细胞衍生的感觉神经元,iPSC-SN)中评估了三种Kv7调节剂——瑞替加滨(Kv7.2至Kv7.5激活剂)、ICA-110381(Kv7.2/Kv7.3特异性激活剂)以及作为对照的ML277(Kv7.1特异性激活剂)对感觉神经元兴奋性的影响。多电极阵列(MEA)记录显示瑞替加滨和ICA-110381可抑制放电(但ML277无此作用),浓度-反应曲线表明瑞替加滨在亚微摩尔浓度下即可使放电减少50%。电流钳记录表明瑞替加滨使iPSC-SN静息电位超极化并提高了阈值。本研究表明Kv7.2/Kv7.3通道是感觉神经元兴奋性的有效调节剂,并表明特异性靶向感觉神经元(包括人类感觉神经元)中Kv7.2/Kv7.3电流的化合物可能提供一种有效的止痛方法。