Nhung Ta Hong, Minh Vu Le, Tuyet Tran Thi, Cuong Thieu Manh, Lam Ngo Le, Trang Hoang Thu, Quy Ngo Xuan, Thong Pham Minh, Thanh Doan Kim, Duc Nguyen Minh
Radiology Center, Vietnam National Cancer Hospital, Hanoi, Vietnam.
Department of Radiology, Hanoi Medical University, Hanoi, Vietnam.
Radiol Case Rep. 2023 Jun 3;18(8):2744-2749. doi: 10.1016/j.radcr.2023.05.032. eCollection 2023 Aug.
Rhabdomyosarcoma (RMS) is the most common mesenchymal tumor in children and adolescents, with 10% of cases occurring in the orbits. RMS should be suspected whenever children present with rapidly progressing unilateral exophthalmos. Its symptoms depend on the lesion's origin and location. We report the clinical case of a 19-year-old male patient admitted to the hospital because of blurred vision and bulging eyes that gradually increased over several months. Magnetic resonance imaging showed a mass located mainly in the left orbit, pushing and deforming but not invading the eyeball. The lesion had grown into the left ethmoid sinus wall. The histopathological incisional biopsy results were with alveolar RMS.
横纹肌肉瘤(RMS)是儿童和青少年中最常见的间叶性肿瘤,10%的病例发生在眼眶。每当儿童出现迅速进展的单侧眼球突出时,应怀疑患有RMS。其症状取决于病变的起源和位置。我们报告一例19岁男性患者的临床病例,该患者因视力模糊和眼球突出数月来逐渐加重而入院。磁共振成像显示一个肿块主要位于左眼眶,推移并使眼球变形但未侵犯眼球。病变已长入左筛窦壁。组织病理学切开活检结果为肺泡型RMS。