Gendvilaitė Neda, Šeinin Dmitrij, Beržanskas Laurynas, Poškus Tomas
Faculty of Medicine, Vilnius University, M. K. Čiurlionio 21, LT-03101, Vilnius, Lithuania.
National Center of Pathology, Affiliate of Vilnius University Hospital Santaros Klinikos, P. Baublio 5, LT-08406 Vilnius, Lithuania.
Acta Med Litu. 2023;30(1):66-73. doi: 10.15388/Amed.2023.30.1.7. Epub 2023 Mar 6.
The solitary fibrous tumor is a rare soft tissue mesenchymal tumor which typically arises from the pleura but may be found anywhere in the body. Abdominal localizations are very rare. The solitary fibrous tumor is classified into two forms, pleural and extrapleural, and morphologically they resemble each other. The diagnostics of the tumor is usually accidental because usually there are no clinical symptoms. The main treatment of the solitary fibrous tumor is the surgical removal of the tumor while radiotherapy treatment and chemotherapy outcomes remain unclear due to the rarity of the tumor and lack of data.
We report the case of the 32-year-old man who was diagnosed with the solitary fibrous tumor of the peritoneal cavity. Laparotomy was performed. A grayish-white, stiff, coarse-grained tumor about 11 cm in diameter of the greater omentum was found and radical omentectomy with tumor removal were performed. Postoperative course was uneventful and the patient is well with no signs of recurrence on the CT scan of the chest and abdomen and MRI of the pelvis at 6 months after surgery.
The solitary fibrous tumor is a rare condition. It is a borderline-malignant tumor but may cause serious complications if not treated. Due to the absence of clinical symptoms, the tumor is usually detected accidentally. The radical surgical removal of the tumor is the most optimal treatment.
孤立性纤维瘤是一种罕见的软组织间叶肿瘤,通常起源于胸膜,但也可能出现在身体的任何部位。腹部定位非常罕见。孤立性纤维瘤分为胸膜型和胸膜外型两种,形态上彼此相似。该肿瘤的诊断通常是偶然的,因为通常没有临床症状。孤立性纤维瘤的主要治疗方法是手术切除肿瘤,而由于肿瘤罕见且缺乏数据,放疗和化疗的效果尚不清楚。
我们报告了一名32岁男性被诊断为腹膜腔孤立性纤维瘤的病例。进行了剖腹手术。发现大网膜上有一个灰白色、质地硬、颗粒状的肿瘤,直径约11厘米,遂行肿瘤切除的根治性网膜切除术。术后过程顺利,术后6个月胸部和腹部CT扫描及骨盆MRI检查显示患者情况良好,无复发迹象。
孤立性纤维瘤是一种罕见疾病。它是一种交界性恶性肿瘤,但如果不治疗可能会引起严重并发症。由于没有临床症状,该肿瘤通常是偶然发现的。肿瘤的根治性手术切除是最理想的治疗方法。