Sugimoto M, Nishikai M, Sato A, Suzuki Y, Nihei M, Uchida J, Mimura N
Ann Rheum Dis. 1987 Feb;46(2):153-5. doi: 10.1136/ard.46.2.153.
Hereditary deficiencies in early and late complement components are well known to predispose to SLE-like syndromes or recurrent infection. Hitherto reported C9 deficient cases have usually been healthy subjects, however, and it is not considered that C9 deficiency is associated with any specific disease. We describe a completely C9 deficient patient with possible Sjögren's syndrome and discuss the relationship.
众所周知，早期和晚期补体成分的遗传性缺陷易引发系统性红斑狼疮样综合征或反复感染。然而，迄今为止报道的C9缺陷病例通常为健康受试者，且人们认为C9缺陷与任何特定疾病均无关联。我们描述了一名可能患有干燥综合征的完全C9缺陷患者，并讨论了二者之间的关系。
