Vita Therapeutics, Baltimore, MD 21043, USA.
Department of Neurology, Baylor College of Medicine, Houston, TX 77030, USA.
Cells. 2024 Mar 29;13(7):596. doi: 10.3390/cells13070596.
Cell therapies derived from induced pluripotent stem cells (iPSCs) offer a promising avenue in the field of regenerative medicine due to iPSCs' expandability, immune compatibility, and pluripotent potential. An increasing number of preclinical and clinical trials have been carried out, exploring the application of iPSC-based therapies for challenging diseases, such as muscular dystrophies. The unique syncytial nature of skeletal muscle allows stem/progenitor cells to integrate, forming new myonuclei and restoring the expression of genes affected by myopathies. This characteristic makes genome-editing techniques especially attractive in these therapies. With genetic modification and iPSC lineage specification methodologies, immune-compatible healthy iPSC-derived muscle cells can be manufactured to reverse the progression of muscle diseases or facilitate tissue regeneration. Despite this exciting advancement, much of the development of iPSC-based therapies for muscle diseases and tissue regeneration is limited to academic settings, with no successful clinical translation reported. The unknown differentiation process in vivo, potential tumorigenicity, and epigenetic abnormality of transplanted cells are preventing their clinical application. In this review, we give an overview on preclinical development of iPSC-derived myogenic cell transplantation therapies including processes related to iPSC-derived myogenic cells such as differentiation, scaling-up, delivery, and cGMP compliance. And we discuss the potential challenges of each step of clinical translation. Additionally, preclinical model systems for testing myogenic cells intended for clinical applications are described.
诱导多能干细胞(iPSC)衍生的细胞疗法由于其可扩展性、免疫相容性和多能性潜力,在再生医学领域提供了有希望的途径。越来越多的临床前和临床试验已经开展,探索基于 iPSC 的疗法在肌肉疾病等挑战性疾病中的应用。骨骼肌的独特合胞特性允许干细胞/祖细胞整合,形成新的肌核并恢复受肌肉疾病影响的基因的表达。这种特性使得基因组编辑技术在这些治疗中特别有吸引力。通过遗传修饰和 iPSC 谱系特异性方法,可以制造出免疫兼容的健康 iPSC 衍生肌肉细胞,以逆转肌肉疾病的进展或促进组织再生。尽管取得了这一令人兴奋的进展,但肌肉疾病和组织再生的 iPSC 疗法的大部分开发仍局限于学术领域,尚未报告成功的临床转化。体内未知的分化过程、移植细胞的潜在致瘤性和表观遗传异常阻碍了它们的临床应用。在这篇综述中,我们概述了 iPSC 衍生的成肌细胞移植疗法的临床前发展,包括与 iPSC 衍生的成肌细胞相关的过程,如分化、规模化、递送和 cGMP 合规性。我们还讨论了临床转化的每个步骤的潜在挑战。此外,还描述了用于测试临床应用的成肌细胞的临床前模型系统。