Elnour Abdelrahman S, Corina Elsadig A, Elnima Mohamed A, Abdelhafeez Abdelhafeez H, Nugud Faisal
National Centre for Pediatric Surgery, Sudan.
Khartoum Teaching Hospital, Sudan.
Int J Surg Case Rep. 2024 Nov;124:110473. doi: 10.1016/j.ijscr.2024.110473. Epub 2024 Oct 16.
Teratomas are germ cell neoplasms arising from the totipotent stem cells. Retroperitoneal teratomas are very rare, accounting for about 5 % of all teratomas of those, primary adrenal ones are exceedingly rare, with few cases reported in the English literature in pediatric age group.
A nine-month-old female presented with a two-month history of gradually increasing abdominal distention, her physical examination revealed a palpable large abdominal mass. Abdominal CT imaging showed a right suprarenal heterogeneous mass. Oncological resection was performed, and histopathology confirmed a primary mature adrenal teratoma.
The diagnosis of primary adrenal teratoma is usually challenging and relies predominantly on imaging studies, and histopathological finding.
Primary adrenal teratoma is extremely rare in pediatric age group, and present a significant diagnostic challenge, as a result it should be considered in the differential diagnosis of pediatric patients with adrenal masses.
畸胎瘤是起源于全能干细胞的生殖细胞肿瘤。腹膜后畸胎瘤非常罕见，约占所有畸胎瘤的5%，其中原发性肾上腺畸胎瘤极为罕见，英文文献中报道的小儿年龄组病例很少。
一名9个月大的女性，有2个月逐渐加重的腹胀病史，体格检查发现可触及一个大的腹部肿块。腹部CT成像显示右肾上腺有一个不均匀肿块。进行了肿瘤切除，组织病理学证实为原发性成熟肾上腺畸胎瘤。
原发性肾上腺畸胎瘤的诊断通常具有挑战性，主要依赖于影像学研究和组织病理学发现。
原发性肾上腺畸胎瘤在小儿年龄组中极为罕见，诊断面临重大挑战，因此在小儿肾上腺肿块患者的鉴别诊断中应予以考虑。
