Montagna P, Medori R, Zappia M, Gallassi R
Ital J Neurol Sci. 1984 Dec;5(4):457-9. doi: 10.1007/BF02042632.
Gowers local panatrophy is a rare disease of skin, subcutaneous and muscular tissues, occurring multifocally and related to the syndromes of congenital or acquired lipodystrophy, although it presents similarities with other connective tissue disorders such as scleroderma. We report here the clinical and electromyographic findings in two patients with local panatrophy and emphasize its benign course and its similarity to scleroderma circumscripta.
高尔斯局部性全身萎缩是一种累及皮肤、皮下组织和肌肉组织的罕见疾病,呈多灶性发生,与先天性或获得性脂肪营养不良综合征相关,尽管它与其他结缔组织疾病如硬皮病有相似之处。我们在此报告两名局部性全身萎缩患者的临床和肌电图检查结果,并强调其良性病程以及与局限性硬皮病的相似性。