一例布希克硬肿病致死病例。
A fatal case of scleredema of Buschke.
作者信息
Sansom J E, Sheehan A L, Kennedy C T, Delaney T J
机构信息
Department of Dermatology, Bristol Royal Infirmary, U.K.
出版信息
Br J Dermatol. 1994 May;130(5):669-70. doi: 10.1111/j.1365-2133.1994.tb13119.x.
Scleredema of Buschke is a rare disorder characterized by the development of areas of skin induration which usually resolve spontaneously. It is occasionally associated with a benign gammopathy, and rarely with myelomatosis. We describe a 60-year-old woman with extensive skin changes, who developed IgA myeloma. Unusually, her skin disease did not respond to conventional myeloma therapy. Death occurred as a consequence of the progressive skin disease.
布施克硬肿病是一种罕见的疾病，其特征是皮肤出现硬结区域，通常可自行消退。它偶尔与良性丙种球蛋白病相关，很少与骨髓瘤相关。我们描述了一名60岁女性，她有广泛的皮肤改变，并发展为IgA骨髓瘤。不同寻常的是，她的皮肤病对传统的骨髓瘤治疗没有反应。死亡是由进行性皮肤病导致的。
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