Bellaiche G, Fontaine H, Choudat L, Lusina D, Ley G, Slama J L
Service de Gastroentérologie, Centre Hospitalier Général Robert-Ballanger, Aulnay-sous-Bois.
Gastroenterol Clin Biol. 1997;21(6-7):519-22.
We report a new case of idiopathic hypereosinophilic syndrome with multivisceral digestive failure. After an erroneous diagnosis of pancreatic cancer, the pathological examination of pancreaticoduodenectomy specimen demonstrated pancreatic fibrosis with eosinophilic infiltration without gastritis or duodenitis. The diagnosis of idiopathic hypereosinophilic syndrome was made three months later upon the classical criteria: a) blood eosinophilia of 1.5 G/L or more, persisting for more than 6 months; b) lack of evidence for any other recognised cause of eosinophilia: c) multiple organ systemic involvement: rheumatologic, cutaneous and digestive (pancreatitis, ascites and diarrhoea): d) previous history of allergic disease and increased plasmatic IgE levels; e) absence of leukemic markers. This case emphasises the difficulty in classifying eosinophilic infiltration of the gut and the possibility of transitional forms between eosinophilic gastro-enteritis and idiopathic hypereosinophilic syndrome. We argue that in case of eosinophilic infiltration of the gut, systematic research of multiple organ systemic involvement is mandatory.
我们报告一例伴有多脏器消化功能衰竭的特发性嗜酸性粒细胞增多综合征新病例。在误诊为胰腺癌后,胰十二指肠切除术标本的病理检查显示胰腺纤维化伴嗜酸性粒细胞浸润,无胃炎或十二指肠炎。三个月后,根据以下经典标准确诊为特发性嗜酸性粒细胞增多综合征:a)血液嗜酸性粒细胞计数≥1.5 G/L,持续超过6个月;b)缺乏其他已知嗜酸性粒细胞增多原因的证据;c)多器官系统受累:风湿性、皮肤和消化系统(胰腺炎、腹水和腹泻);d)既往有过敏性疾病史且血浆IgE水平升高;e)无白血病标志物。该病例强调了肠道嗜酸性粒细胞浸润分类的困难以及嗜酸性胃肠炎和特发性嗜酸性粒细胞增多综合征之间存在过渡形式的可能性。我们认为,对于肠道嗜酸性粒细胞浸润病例,必须系统研究多器官系统受累情况。