Govender D, Pillay P
Department of Anatomical Pathology, University of Natal Medical School, Congella, Durban, South Africa.
Arch Pathol Lab Med. 1998 Aug;122(8):740-2.
We report a unique case of primary myxoid liposarcoma of the floor of the mouth, in which well-differentiated rhabdomyoblasts were present. The tumor was incompletely excised. The patient is free of recurrence or metastasis following a course of radiotherapy. Heterologous components found in a liposarcoma include leiomyosarcoma, rhabdomyosarcoma, chondrosarcoma, osteosarcoma, and angiosarcoma. These elements have been described mainly in dedifferentiated liposarcomas situated in the retroperitoneum. To our knowledge, there has been only one report of a liposarcoma with rhabdomyosarcomatous differentiation occurring in the absence of a dedifferentiated component. The clinical implications of the presence of heterologous components without dedifferentiation are unclear.
我们报告了一例罕见的口底原发性黏液样脂肪肉瘤病例，其中存在分化良好的横纹肌母细胞。肿瘤切除不完全。患者在接受一个疗程的放射治疗后未出现复发或转移。脂肪肉瘤中发现的异源性成分包括平滑肌肉瘤、横纹肌肉瘤、软骨肉瘤、骨肉瘤和血管肉瘤。这些成分主要在位于腹膜后的去分化脂肪肉瘤中被描述。据我们所知，仅有一篇关于无去分化成分的具有横纹肌肉瘤分化的脂肪肉瘤的报道。未发生去分化的异源性成分的临床意义尚不清楚。
