Serafini Barbara, Rosicarelli Barbara, Magliozzi Roberta, Stigliano Egidio, Aloisi Francesca
Department of Cell Biology and Neuroscience, Istituto Superiore di Sanità, Viale Regina Elena 299, 00161 Roma, Italy.
Brain Pathol. 2004 Apr;14(2):164-74. doi: 10.1111/j.1750-3639.2004.tb00049.x.
Multiple sclerosis (MS) is characterized by synthesis of oligoclonal immunoglobulins and the presence of B-cell clonal expansions in the central nervous system (CNS). Because ectopic lymphoid tissue generated at sites of chronic inflammation is thought to be important in sustaining immunopathological processes, we have investigated whether structures resembling lymphoid follicles could be identified in the CNS of MS patients. Sections from post-mortem MS brains and spinal cords were screened using immunohistochemistry for the presence of CD20+ B-cells, CD3+ T-cells, CD138+ plasma cells and CD21+, CD35+ follicular dendritic cells, and for the expression of lymphoid chemokines (CXCL 13, CCL21) and peripheral node addressin (PNAd). Lymphoid follicle-like structures containing B-cells, T-cells and plasma cells, and a network of follicular dendritic cells producing CXCL13 were observed in the cerebral meninges of 2 out of 3 patients with secondary progressive MS, but not in relapsing remitting and primary progressive MS. We also show that proliferating B-cells are present in intrameningeal follicles, a finding which is suggestive of germinal center formation. No follicle-like structures were detected in parenchymal lesions. The formation of ectopic lymphoid follicies in the meninges of patients with MS could represent a critical step in maintaining humoral autoimmunity and in disease exacerbation.
多发性硬化症(MS)的特征是中枢神经系统(CNS)中寡克隆免疫球蛋白的合成以及B细胞克隆性扩增的存在。由于慢性炎症部位产生的异位淋巴组织被认为在维持免疫病理过程中很重要,我们研究了是否能在MS患者的CNS中识别出类似淋巴滤泡的结构。使用免疫组织化学方法对死后MS脑和脊髓切片进行筛查,以检测CD20 + B细胞、CD3 + T细胞、CD138 +浆细胞以及CD21 +、CD35 +滤泡树突状细胞的存在,并检测淋巴趋化因子(CXCL 13、CCL21)和外周淋巴结地址素(PNAd)的表达。在3例继发进展型MS患者中的2例的脑膜中观察到含有B细胞、T细胞和浆细胞的类淋巴滤泡结构,以及产生CXCL13的滤泡树突状细胞网络,但在复发缓解型和原发进展型MS中未观察到。我们还表明,增殖的B细胞存在于脑膜内滤泡中,这一发现提示生发中心的形成。在实质病变中未检测到类滤泡结构。MS患者脑膜中异位淋巴滤泡的形成可能是维持体液自身免疫和疾病加重的关键步骤。