Kim Cheol Hong, Kim Yoon Ha, Cho Moon Kyoung, Kim Ki Min, Ha Jin A, Joo Eun Hyun, Kim Seok Mo, Song Tae-Bok
Department of Obstetrics and Gynecology, Chonnam National University, College of Medicine, 8 Hak-dong, Dong-gu, Gwangju, Korea.
J Korean Med Sci. 2007 Apr;22(2):357-61. doi: 10.3346/jkms.2007.22.2.357.
Although congenital renal tumors are rare, congenital mesoblastic nephroma (CMN) is the most common renal tumor in early infancy. It is non-metastatic, well differentiated, amenable to surgical removal, and carries a good prognosis. Polyhydramnios has been detected in most of the published cases of CMN. However, we experienced a rare case of fetal CMN associated with oligohydramnios. A 28-yr old woman at 34 weeks of gestation was referred to our hospital for oligohydramnios and a fetal abdominal mass. An ultrasonography revealed a huge, well-encapsulated mass arising from the right kidney. An emergency cesarean section was performed due to fetal distress. After birth, despite intensive neonatal care, the baby died because of renal failure, disseminated intravascular coagulopathy, pulmonary edema, together with other problems.
虽然先天性肾肿瘤很少见,但先天性中胚层肾瘤(CMN)是婴儿早期最常见的肾肿瘤。它不发生转移,分化良好,适合手术切除,预后良好。在大多数已发表的CMN病例中都检测到羊水过多。然而,我们遇到了一例罕见的与羊水过少相关的胎儿CMN病例。一名28岁、妊娠34周的女性因羊水过少和胎儿腹部肿块被转诊至我院。超声检查显示右肾有一个巨大的、包膜完整的肿块。由于胎儿窘迫,进行了紧急剖宫产。出生后,尽管给予了 intensive neonatal care,但婴儿因肾衰竭、弥散性血管内凝血、肺水肿及其他问题而死亡。