Abenza-Abildua Maria Jose, Fuentes Blanca, Diaz Domingo, Royo Aranzazu, Olea Teresa, Aguilar-Amat Maria Jose, Diez-Tejedor Exuperio
Hospital Universitario La Paz, Neurology, Paseo de la Castellana 261, Madrid, 28046, Spain.
BMJ Case Rep. 2009;2009. doi: 10.1136/bcr.07.2008.0467. Epub 2009 May 25.
Reversible posterior leukoencephalopathy syndrome (RPLS) is a clinical radiological syndrome, characterised by acute headache, altered consciousness, seizures and hypertension. The most frequent causes are hypertensive encephalopathy, eclampsia and some immunosuppressive therapies. The pathogenesis remains unclear, but it appears to be related to altered cerebral circulation, producing oedema that can be seen on MRI, and it resolves in 2 or 3 weeks. In the present report, a possible first reported case of cyclophosphamide-induced RPLS in a 27-year-old man with high blood pressure (HBP) and glomerulonephritis caused by Goodpasture syndrome, treated with cyclophosphamide during the last month and prednisone for glomerulonephritis resulting from Goodpasture syndrome without other immunosuppressive drugs, is described.Symptoms appeared during a hypertensive crisis, but when cyclophosphamide was replaced by rituximab and hypertension was controlled, the patient did not have neurological symptoms. Almost all reported cases induced by immunosuppressive therapy or other causes were associated with hypertension as well.
可逆性后部白质脑病综合征(RPLS)是一种临床放射学综合征,其特征为急性头痛、意识改变、癫痫发作和高血压。最常见的病因是高血压脑病、子痫和一些免疫抑制疗法。其发病机制尚不清楚,但似乎与脑循环改变有关,可产生MRI上可见的水肿,且在2至3周内消退。在本报告中,描述了一例可能为首报的环磷酰胺诱发的RPLS病例,患者为一名27岁男性,患有高血压(HBP)和由Goodpasture综合征引起的肾小球肾炎,上个月接受了环磷酰胺治疗,因Goodpasture综合征导致的肾小球肾炎接受泼尼松治疗,未使用其他免疫抑制药物。症状出现在高血压危象期间,但当环磷酰胺被利妥昔单抗替代且高血压得到控制后,患者未出现神经症状。几乎所有由免疫抑制疗法或其他原因诱发的报告病例也都与高血压有关。