Tehran University of Medical Sciences, Aliasghar Childrens Hospital, Tehran, Iran.
Rheumatol Int. 2012 Sep;32(9):2933-5. doi: 10.1007/s00296-011-2028-2. Epub 2011 Jul 27.
Juvenile dermatomyositis (JDM) is a rare autoimmune disease characterized by proximal muscle weakness, skin lesions, gastro intestinal, pulmonary, cardiac and small nerve damage. Renal involvement has been rarely reported in JDM. This is the report of a 7-year-old boy presented with nephrotic syndrome (NS) and subsequent renal failure. Clinical manifestations of JDM appeared gradually. Renal manifestations could be considered as a rare initial presentation of JDM.
幼年型皮肌炎（JDM）是一种罕见的自身免疫性疾病，其特征是近端肌肉无力、皮肤损伤、胃肠道、肺部、心脏和小神经损伤。JDM 中肾脏受累很少见。本文报告了一例 7 岁男孩，表现为肾病综合征（NS）和随后的肾衰竭。JDM 的临床表现逐渐出现。肾脏表现可被认为是 JDM 的罕见首发表现。
