Department of Neuroscience, Yale University, New Haven, CT, USA.
Department of Pathology, Yale University, New Haven, CT, USA.
Nat Commun. 2023 May 5;14(1):2589. doi: 10.1038/s41467-023-37025-7.
Due to commonalities in pathophysiology, age-related macular degeneration (AMD) represents a uniquely accessible model to investigate therapies for neurodegenerative diseases, leading us to examine whether pathways of disease progression are shared across neurodegenerative conditions. Here we use single-nucleus RNA sequencing to profile lesions from 11 postmortem human retinas with age-related macular degeneration and 6 control retinas with no history of retinal disease. We create a machine-learning pipeline based on recent advances in data geometry and topology and identify activated glial populations enriched in the early phase of disease. Examining single-cell data from Alzheimer's disease and progressive multiple sclerosis with our pipeline, we find a similar glial activation profile enriched in the early phase of these neurodegenerative diseases. In late-stage age-related macular degeneration, we identify a microglia-to-astrocyte signaling axis mediated by interleukin-1β which drives angiogenesis characteristic of disease pathogenesis. We validated this mechanism using in vitro and in vivo assays in mouse, identifying a possible new therapeutic target for AMD and possibly other neurodegenerative conditions. Thus, due to shared glial states, the retina provides a potential system for investigating therapeutic approaches in neurodegenerative diseases.
由于病理生理学的共同性,年龄相关性黄斑变性 (AMD) 代表了一个特别适合研究神经退行性疾病治疗方法的模型,这促使我们研究疾病进展的途径是否在神经退行性疾病中共享。在这里,我们使用单细胞 RNA 测序来分析 11 个人类 AMD 尸检后视网膜病变和 6 个无视网膜疾病史的对照视网膜病变的病变。我们基于数据几何和拓扑学的最新进展创建了一个机器学习管道,并鉴定了在疾病早期富集的激活神经胶质群体。我们使用该管道检查来自阿尔茨海默病和进行性多发性硬化症的单细胞数据,发现这些神经退行性疾病早期也存在类似的神经胶质激活特征。在晚期 AMD 中,我们鉴定了由白细胞介素 1β介导的小胶质细胞到星形胶质细胞信号轴,该信号轴驱动疾病发病机制的血管生成。我们使用小鼠的体外和体内试验验证了这种机制,为 AMD 和可能其他神经退行性疾病确定了一个可能的新治疗靶点。因此,由于共享的神经胶质状态,视网膜为研究神经退行性疾病的治疗方法提供了一个潜在的系统。