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一名患有主动脉周围静脉环的患者出现双胡桃夹综合征:一例罕见病例报告。

Double nutcracker syndrome in a patient with circumaortic venous ring: a rare case report.

作者信息

Farina Renato, Foti Pietro Valerio, Nicolosi Lorena, Basile Antonio

机构信息

Department of Medical and Surgical Sciences and Advanced Technologies "GF Ingrassia", University of Catania, Catania, Italy.

出版信息

J Ultrason. 2023 May 11;23(93):e101-e105. doi: 10.15557/jou.2023.0018. eCollection 2023 Jun.

DOI:10.15557/jou.2023.0018
PMID:37520751
原文链接:https://pmc.ncbi.nlm.nih.gov/articles/PMC10379846/
Abstract

AIM OF THE STUDY

In this article, we describe a rare case of the nutcracker syndrome caused by combined compression of the left anteroaortic and retroaortic renal veins. A 42-year-old woman presented with microhematuria and left flank pain. The patient underwent computed tomography and Doppler ultrasound which showed the left renal veins with anteroaortic and retroaortic courses, with signs of compression. Compression of the anteroaortic renal vein was caused by a narrowing of the aortomesenteric space, whereas compression of the retroaortic renal vein was caused by a narrowing of the aortovertebral space.

CONCLUSIONS

NCS is a rare disease, poorly understood and difficult to diagnose mainly due to the non-specificity of symptoms. Imaging is essential for diagnosis, and the combination of ultrasound and computed tomography allows for better classification of the disease. Increased disclosure of these cases can significantly contribute to a reduction of false negatives.

摘要

研究目的

在本文中,我们描述了一例罕见的胡桃夹综合征,由左肾静脉前主动脉段和主动脉后段联合受压引起。一名42岁女性出现镜下血尿和左侧腰痛。患者接受了计算机断层扫描和多普勒超声检查,结果显示左肾静脉走行于主动脉前方和后方,并有受压迹象。主动脉前肾静脉受压是由于主动脉肠系膜间隙变窄所致,而主动脉后肾静脉受压是由于主动脉椎体间隙变窄所致。

结论

胡桃夹综合征是一种罕见疾病,由于症状不具特异性,人们对其了解甚少且难以诊断。影像学检查对诊断至关重要,超声和计算机断层扫描相结合有助于对该疾病进行更好的分类。增加对这些病例的认识可显著减少假阴性结果。

https://cdn.ncbi.nlm.nih.gov/pmc/blobs/6e79/10379846/5d36e4121982/j_jou.2023.0018_fig_003.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/6e79/10379846/8a503adacc92/j_jou.2023.0018_fig_001.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/6e79/10379846/adf3ae228331/j_jou.2023.0018_fig_002.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/6e79/10379846/5d36e4121982/j_jou.2023.0018_fig_003.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/6e79/10379846/8a503adacc92/j_jou.2023.0018_fig_001.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/6e79/10379846/adf3ae228331/j_jou.2023.0018_fig_002.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/6e79/10379846/5d36e4121982/j_jou.2023.0018_fig_003.jpg

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本文引用的文献

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Nutcracker Phenomenon: A Rare Incidental Finding.胡桃夹现象:一种罕见的偶然发现。
Cureus. 2022 Dec 22;14(12):e32822. doi: 10.7759/cureus.32822. eCollection 2022 Dec.
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Intravascular Ultrasound Guidance Is Associated with a Favorable One-Year Target Vessel Failure Rate and No Residual Myocardial Ischemia after the Percutaneous Treatment of Very Long Coronary Artery Lesions.血管内超声引导与超长冠状动脉病变经皮治疗后一年的靶血管失败率较低且无残余心肌缺血相关。
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Endovascular treatment of nutcracker syndrome.
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Nutcracker syndrome: diagnosis and therapy.胡桃夹综合征:诊断与治疗
Cardiovasc Diagn Ther. 2021 Oct;11(5):1140-1149. doi: 10.21037/cdt-20-160.
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Superior mesenteric artery syndrome (Wilkie Syndrome) with unusual clinical onset: Description of a rare case.肠系膜上动脉综合征(威尔基综合征)伴不寻常临床起病:1例罕见病例报道
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Pelvic Venous Congestion Secondary to a Circumaortic Renal Collar in an Adolescent Female: Report of a Case.青少年女性因主动脉周围肾环导致的盆腔静脉淤血:一例报告
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Posterior nutcracker syndrome: a case report.胡桃夹综合征:一例报告。
J Med Case Rep. 2021 Feb 1;15(1):42. doi: 10.1186/s13256-020-02617-0.
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A Case of Nutcracker Syndrome Combined with Wilkie Syndrome with Unusual Clinical Presentation.胡桃夹综合征合并 Wilkie 综合征 1 例:罕见临床表现
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A systematic review on management of nutcracker syndrome.胡桃夹综合征的治疗方法的系统评价。
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