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克雅氏病:与库鲁病的更多相似之处。

Creutzfeldt-Jakob disease: further similarities with kuru.

作者信息

Adams H, Beck E, Shenkin A M

出版信息

J Neurol Neurosurg Psychiatry. 1974 Feb;37(2):195-200. doi: 10.1136/jnnp.37.2.195.

DOI:10.1136/jnnp.37.2.195
PMID:4362244
原文链接:https://pmc.ncbi.nlm.nih.gov/articles/PMC494608/
Abstract

A typical case of Creutzfeldt-Jakob disease is described. Two unusual morphological features-namely, `kuru-like' plaques in the cerebellum and coarsely vacuolated neurones in the striatum-are further similarities between Creutzfeldt-Jakob disease and kuru.

摘要

本文描述了一例典型的克雅氏病病例。克雅氏病与库鲁病之间存在另外两个相似之处,即小脑出现“类库鲁病”斑块以及纹状体神经元出现粗大空泡化。

https://cdn.ncbi.nlm.nih.gov/pmc/blobs/ca4e/494608/25a7e95475b4/jnnpsyc00188-0079-a.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/ca4e/494608/0e2a89aa2597/jnnpsyc00188-0076-a.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/ca4e/494608/fea279b76d6d/jnnpsyc00188-0076-b.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/ca4e/494608/7da712d85e1b/jnnpsyc00188-0076-c.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/ca4e/494608/131d4bd74919/jnnpsyc00188-0077-a.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/ca4e/494608/cbe0fd3f9ace/jnnpsyc00188-0078-a.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/ca4e/494608/05b411014fd6/jnnpsyc00188-0078-b.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/ca4e/494608/25a7e95475b4/jnnpsyc00188-0079-a.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/ca4e/494608/0e2a89aa2597/jnnpsyc00188-0076-a.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/ca4e/494608/fea279b76d6d/jnnpsyc00188-0076-b.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/ca4e/494608/7da712d85e1b/jnnpsyc00188-0076-c.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/ca4e/494608/131d4bd74919/jnnpsyc00188-0077-a.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/ca4e/494608/cbe0fd3f9ace/jnnpsyc00188-0078-a.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/ca4e/494608/05b411014fd6/jnnpsyc00188-0078-b.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/ca4e/494608/25a7e95475b4/jnnpsyc00188-0079-a.jpg

相似文献

1
Creutzfeldt-Jakob disease: further similarities with kuru.克雅氏病:与库鲁病的更多相似之处。
J Neurol Neurosurg Psychiatry. 1974 Feb;37(2):195-200. doi: 10.1136/jnnp.37.2.195.
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Creutzfeldt-Jakob disease. Some unusual morphological features reminiscent of kuru.
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An autopsy case of Creutzfeldt-Jakob disease with kuru-like neuropathological changes.一例具有库鲁病样神经病理学改变的克雅氏病尸检病例。
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Experimental kuru in the chimpanzee. A neuropathological study.黑猩猩的实验性库鲁病。一项神经病理学研究。
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Creutzfeldt-Jakob disease. An autopsy case of the panencephalopathic type and a review of the literature.克雅氏病。全脑病变型尸检病例及文献综述。
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Kuru plaques in the brain of two cases with Creutzfeldt-Jakob disease. A common origin for the two diseases?两例克雅氏病患者大脑中的库鲁病斑块。这两种疾病有共同起源吗?
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Case records of the Massachusetts General Hospital. Weekly clinicopathological exercises. Case 45-1980.
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Kuru and Creutzfeldt-Jakob disease: clinical and aetiological aspects.
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引用本文的文献

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Creutzfeldt-Jakob Disease Misdiagnosed as Multiple System Atrophy.被误诊为多系统萎缩的克雅氏病
Mov Disord Clin Pract. 2023 Jan 20;10(3):496-500. doi: 10.1002/mdc3.13654. eCollection 2023 Mar.
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Gerstmann-Sträussler-Scheinker's disease. Electron-microscopic observations on a brain biopsy.格斯特曼-施特劳斯勒-谢inker病。脑活检的电子显微镜观察
Acta Neuropathol. 1980;52(3):203-11. doi: 10.1007/BF00705808.
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[Morbus Gerstmann-Sträussler-Scheinker. The Sch. family-a report of three cases (author's transl)].[格斯特曼-施特劳斯勒-申克病。施氏家族——三例报告(作者译)]

本文引用的文献

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AN ATAXIC FORM OF SUBACUTE PRESENILE POLIOENCEPHALOPATHY (CREUTZFELDT-JAKOB DISEASE).一种亚急性早老性脑脊髓病(克雅氏病)的共济失调型
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The ataxic (cerebellar) form of Creutzfeldt-Jakob disease.克雅氏病的共济失调(小脑)型
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Creutzfeldt-Jakob disease. Some unusual morphological features reminiscent of kuru.
Z Neurol. 1973 Dec 31;206(1):1-24.
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Cerebellar plaques in familial Alzheimer's disease (Gerstmann-Sträussler-Scheinker variant?).家族性阿尔茨海默病中的小脑斑块(格斯特曼-施特劳斯勒-谢因克变异型?)
Acta Neuropathol. 1985;65(3-4):235-46. doi: 10.1007/BF00687003.
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PrP amyloid plaques in Creutzfeldt-Jakob disease of short duration: immunohistochemical studies of 5 cases from Poland.短期克雅氏病中的朊蛋白淀粉样斑块:来自波兰的5例病例的免疫组织化学研究
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Kuru-plaques in a case of Creutzfeldt-Jakob disease.
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Creutzfeldt-Jakob disease.克雅氏病
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Spongiform virus encephalopathies.海绵状病毒脑病
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