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皮肤胶原性血管病

Cutaneous Collagenous Vasculopathy.

作者信息

Brady Bobbi Georgia, Ortleb Melanie, Boyd Alan S, Powers Jennifer

机构信息

Vanderbilt University.

出版信息

J Clin Aesthet Dermatol. 2015 Nov;8(11):49-52.

Abstract

Cutaneous collagenous vasculopathy is a rare microangiopathy of dermal blood vessels. Clinically indistinguishable from generalized essential telangiectasia, this condition is diagnosed by its unique histological appearance. In contrast to other primary telangiectatic processes, cutaneous collagenous vasculopathy has dilated vascular structures that contain deposits of eosinophilic hyaline material within the vessel walls. To date, cutaneous collagenous vasculopathy has been described in a total of 19 cases in the medical literature. The first several cases were described exclusively in middle-aged to elderly men. Though it has now been described in both men and women, cutaneous collagenous vasculopathy is still most often described in middle-aged to older adults. No particular disease or medication has been linked to the development of cutaneous collagenous vasculopathy, and the etiology remains unknown. In this case series, the authors present three additional patients diagnosed with cutaneous collagenous vasculopathy and discuss their clinical and histopathologic features.

摘要

皮肤胶原性血管病是一种罕见的真皮血管微血管病。临床上与全身性特发性毛细血管扩张难以区分,该病通过其独特的组织学表现得以诊断。与其他原发性毛细血管扩张性疾病不同,皮肤胶原性血管病的血管结构扩张,血管壁内含有嗜酸性透明物质沉积。迄今为止,医学文献中总共描述了19例皮肤胶原性血管病。最初的几例仅在中年至老年男性中被描述。尽管现在已在男性和女性中均有描述,但皮肤胶原性血管病仍最常出现在中年至老年成年人中。没有特定疾病或药物与皮肤胶原性血管病的发生有关,其病因仍然不明。在这个病例系列中,作者介绍了另外三名被诊断为皮肤胶原性血管病的患者,并讨论了他们的临床和组织病理学特征。

相似文献

1
Cutaneous Collagenous Vasculopathy.皮肤胶原性血管病
J Clin Aesthet Dermatol. 2015 Nov;8(11):49-52.
2
Cutaneous collagenous vasculopathy: a rare cutaneous microangiopathy.皮肤胶原性血管病:一种罕见的皮肤微血管病。
J Cutan Pathol. 2012 Aug;39(8):741-6. doi: 10.1111/j.1600-0560.2012.01936.x. Epub 2012 Jul 16.
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Cutaneous collagenous vasculopathy: A rare case report.皮肤胶原性血管病:一例罕见病例报告。
Indian Dermatol Online J. 2016 Jan-Feb;7(1):40-2. doi: 10.4103/2229-5178.174327.
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A rare case of cutaneous collagenous vasculopathy.一例罕见的皮肤胶原性血管病。
Australas J Dermatol. 2016 Aug;57(3):e97-9. doi: 10.1111/ajd.12330. Epub 2015 Apr 15.

引用本文的文献

1
Dermoscopic Features of Cutaneous Collagenous Vasculopathy: A Report of Rare Disorder.
Indian Dermatol Online J. 2018 Sep-Oct;9(5):342-344. doi: 10.4103/idoj.IDOJ_114_17.

本文引用的文献

1
Cutaneous collagenous vasculopathy: report of a case.皮肤胶原性血管病:一例报告
Clin Exp Dermatol. 2014 Mar;39(2):228-30. doi: 10.1111/ced.12258. Epub 2014 Jan 23.
3
Cutaneous collagenous vasculopathy.
J Cutan Pathol. 2013 May;40(5):524. doi: 10.1111/cup.12092. Epub 2013 Feb 4.
7
Cutaneous collagenous vasculopathy: a rare cutaneous microangiopathy.皮肤胶原性血管病:一种罕见的皮肤微血管病。
J Cutan Pathol. 2012 Aug;39(8):741-6. doi: 10.1111/j.1600-0560.2012.01936.x. Epub 2012 Jul 16.
10
Cutaneous collagenous vasculopathy.
J Am Acad Dermatol. 2011 Jun;64(6):1179-80. doi: 10.1016/j.jaad.2010.11.047.

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