Scuderi G, Verboschi F, Domanico D, Spadea L
Ophthalmology Unit, NESMOS Department, Sant'Andrea Hospital, "Sapienza" University of Rome, Via di Grottarossa 1035-1039, 00189 Rome, Italy.
Department of Ophthalmology, A. Fiorini Hospital, "Sapienza" University of Rome, Via Firenze, 04019 Terracina, Italy.
Case Rep Med. 2016;2016:4264829. doi: 10.1155/2016/4264829. Epub 2016 Apr 24.
Stargardt disease is the most common hereditary macular degeneration in juveniles. It is characterized by macular dystrophy associated with loss of central vision in the first or second decade of life, a "beaten-metal" appearance in the fovea or parafoveal region, yellowish flecks around the macula or in posterior area of the retina, progressive atrophy of the bilateral foveal retinal pigment epithelium, and the "dark choroid" sign on fundus fluorescein angiography in most cases. We report a case of Stargardt disease in a 26-year-old Caucasian female submitted to rehabilitative training with microperimetry MP-1 to find a new preferred retinal locus (PRL) and to train her to better her quality of life. Best corrected visual acuity, mean retinal sensitivity, fixation, bivariate contour ellipse area, and speed reading were evaluated before and after the training and results were discussed.
斯塔加特病是青少年中最常见的遗传性黄斑变性。其特征为黄斑营养不良,在生命的第一个或第二个十年出现中心视力丧失,中央凹或旁中央凹区域有“ beaten - metal”外观,黄斑周围或视网膜后部区域有淡黄色斑点,双侧中央凹视网膜色素上皮进行性萎缩,且在大多数情况下眼底荧光血管造影有“暗脉络膜”征。我们报告一例26岁的白种女性斯塔加特病患者,接受了使用MP - 1微视野计的康复训练,以找到新的最佳视网膜位点(PRL)并训练她改善生活质量。在训练前后评估了最佳矫正视力、平均视网膜敏感度、注视、双变量轮廓椭圆面积和快速阅读情况,并对结果进行了讨论。