Ono J, Sakoda K, Akita H
Ann Surg. 1982 Feb;195(2):203-8. doi: 10.1097/00000658-198202000-00014.
Twenty-two cholangiograms of adults with congenital dilatation of the common bile duct were studied and analyzed. Diagnosis of this disease was established by endoscopic retrograde cholangiopancreaticography in nine patients, by percutaneous transhepatic cholangiography in two patients, and by operative cholangiography in 11 patients. All patients, except one with Caroli's disease, were classified as type I according to Alonso-Lej. An anomalous junction of the pancreaticobiliary ductal system (AJPBDS) was observed in 15 cases. In nine patients the common bile duct joined the main pancreatic duct, and in the remaining six patients, the pancreatic duct was noted to join the common bile duct. These anomalies are considered to be an important etiologic factor in the development of choledochal dilatation. Total cyst excision and hepaticojejunostomy in a Roux-en-Y fashion is recommended as the procedure of choice in those cases with AJPBDS. This is based on the high incidence of cholangitis and the high propensity to induce malignancy of cystic wall following simple drainage.
对22例成人先天性胆总管扩张患者的胆管造影进行了研究和分析。9例患者通过内镜逆行胰胆管造影术确诊该病,2例患者通过经皮肝穿刺胆管造影术确诊,11例患者通过手术胆管造影术确诊。除1例卡洛里病患者外,所有患者根据阿隆索 - 莱伊分类为I型。15例观察到胰胆管系统异常连接(AJPBDS)。9例患者胆总管与主胰管相连,其余6例患者胰管与胆总管相连。这些异常被认为是胆总管扩张发展的重要病因。对于有AJPBDS的病例,建议采用Roux-en-Y式全囊肿切除和肝空肠吻合术作为首选手术。这是基于胆管炎的高发病率以及单纯引流后囊肿壁诱发恶性肿瘤的高倾向。